L-Homocitrulline (Synonyms: ε-Carbamyllysine, L-Epsilon-Amino-Carbamoyl-Lysine, L-Homocitrulline, NSC 27428) |
رقم الكتالوجGC31587 |
يتم استقلاب L-Homocitrulline إلى homoarginine من خلال homoargininosuccinate عبر مسار دورة اليوريا ويمكن أن يؤدي خلل التمثيل الغذائي إلى عدم تحمل بروتين ليسينوريك (LPI)
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Cas No.: 1190-49-4
Sample solution is provided at 25 µL, 10mM.
L-Homocitrulline is metabolized to homoarginine through homoargininosuccinate via the urea cycle pathway and its metabolic abnormality could lead to Lysinuric Protein Intolerance (LPI).
[1]. Kato T, et al. Homocitrullinuria and homoargininuria in lysinuric protein intolerance. J Inherit Metab Dis. 1989;12(2):157-61.
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