H-HoPro-OH |
Katalog-Nr.GC31403 |
H-HoPro-OH (H-HoPro-OH) ist ein Abbauprodukt von Lysin, das sich in KÖrperflÜssigkeiten von SÄuglingen mit generalisierten genetischen peroxisomalen StÖrungen, wie Zellweger-Syndrom, neonataler Adrenoleukodystrophie, anreichert.
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Cas No.: 3105-95-1
Sample solution is provided at 25 µL, 10mM.
H-HoPro-OH is a breakdown product of lysine, accumulates in body fluids of infants with generalized genetic peroxisomal disorders, such as Zellweger syndrome, neonatal adrenoleukodystrophy.
[1]. Mihalik SJ, et al. Peroxisomal L-pipecolic acid oxidation is deficient in liver from Zellweger syndrome patients. Pediatr Res. 1989 May;25(5):548-52.
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